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Title: | Heart failure in cardiomyopathies: a position paper from the Heart Failure Association of the European Society of Cardiology | Authors: | Seferovic, Petar M. Polovina, Marija Bauersachs, Johann Arad, Michael Ben Gal, Tuvia Lund, Lars H. Felix, Stephan B. Arbustini, Eloisa Caforio, Alida L. P. Farmakis, Dimitrios Filippatos, Gerasimos S. Gialafos, Elias Kanjuh, Vladimir Krljanac, Gordana Limongelli, Giuseppe Linhart, Ales Lyon, Alexander R. Maksimovic, Ruzica Milicic, Davor Milinkovic, Ivan Noutsias, Michel Oto, Ali Oto, Oztekin Pavlovic, Sinisa U. Piepoli, Massimo F. Ristic, Arsen D. Rosano, Giuseppe M. C. Seggewiss, Hubert Asanin, Milika Seferovic, Jelena R. Ruschitzka, Frank Celutkiene, Jelena Jaarsma, Tiny Mueller, Christian Moura, Brenda Hill, Loreena Volterrani, Maurizio Lopatin, Yuri Metra, Marco Backs, Johannes MULLENS, Wilfried Chioncel, Ovidiu de Boer, Rudolf A. Anker, Stefan Rapezzi, Claudio Coats, Andrew J. s Tschoepes, Carsten |
Issue Date: | 2019 | Publisher: | WILEY | Source: | EUROPEAN JOURNAL OF HEART FAILURE, 21(5), p. 553-576 | Abstract: | Cardiomyopathies are a heterogeneous group of heart muscle diseases and an important cause of heart failure (HF). Current knowledge on incidence, pathophysiology and natural history of HF in cardiomyopathies is limited, and distinct features of their therapeutic responses have not been systematically addressed. Therefore, this position paper focuses on epidemiology, pathophysiology, natural history and latest developments in treatment of HF in patients with dilated (DCM), hypertrophic (HCM) and restrictive (RCM) cardiomyopathies. In DCM, HF with reduced ejection fraction (HFrEF) has high incidence and prevalence and represents the most frequent cause of death, despite improvements in treatment. In addition, advanced HF in DCM is one of the leading indications for heart transplantation. In HCM, HF with preserved ejection (HFpEF) affects most patients with obstructive, and similar to 10% of patients with non-obstructive HCM. A timely treatment is important, since development of advanced HF, although rare in HCM, portends a poor prognosis. In RCM, HFpEF is common, while HFrEF occurs later and more frequently in amyloidosis or iron overload/haemochromatosis. Irrespective of RCM aetiology, HF is a harbinger of a poor outcome. Recent advances in our understanding of the mechanisms underlying the development of HF in cardiomyopathies have significant implications for therapeutic decision-making. In addition, new aetiology-specific treatment options (e.g. enzyme replacement therapy, transthyretin stabilizers, immunoadsorption, immunotherapy, etc.) have shown a potential to improve outcomes. Still, causative therapies of many cardiomyopathies are lacking, highlighting the need for the development of effective strategies to prevent and treat HF in cardiomyopathies. | Notes: | [Seferovic, Petar M.; Polovina, Marija; Krljanac, Gordana; Maksimovic, Ruzica; Pavlovic, Sinisa U.; Ristic, Arsen D.; Asanin, Milika; Seferovic, Jelena R.] Univ Belgrade, Fac Med, 8 Koste Todorovica, Belgrade 11000, Serbia. [Seferovic, Petar M.; Kanjuh, Vladimir] Serbian Acad Arts & Sci, Belgrade, Serbia. [Polovina, Marija; Krljanac, Gordana; Milinkovic, Ivan; Ristic, Arsen D.; Asanin, Milika] Clin Ctr Serbia, Dept Cardiol, Belgrade, Serbia. [Bauersachs, Johann] Med Sch Hannover, Dept Cardiol & Angiol, Hannover, Germany. [Arad, Michael] Tel Aviv Univ, Sheba Med Ctr, Leviev Heart Ctr, Cardiomyopathy Clin, Tel Aviv, Israel. [Arad, Michael] Tel Aviv Univ, Sheba Med Ctr, Leviev Heart Ctr, Heart Failure Inst, Tel Aviv, Israel. [Arad, Michael] Tel Aviv Univ, Sackler Sch Med, Tel Aviv, Israel. [Ben Gal, Tuvia] Tel Aviv Univ, Sackler Fac Med, Rabin Med Ctr, Dept Cardiol, Tel Aviv, Israel. [Lund, Lars H.] Karolinska Univ Hosp, Karolinska Inst, Dept Med, Stockholm, Sweden. [Lund, Lars H.] Karolinska Univ Hosp, Heart & Vasc Theme, Stockholm, Sweden. [Felix, Stephan B.] Univ Med Greifswald, Dept Internal Med B, Greifswald, Germany. [Arbustini, Eloisa] Univ Hosp Policlin San Matteo, IRCCS Fdn, Ctr Inherited Cardiovasc Dis, Pavia, Italy. [Caforio, Alida L. P.] Univ Padua, Dept Cardiol Thorac & Vasc Sci, Padua, Italy. [Farmakis, Dimitrios; Filippatos, Gerasimos S.] Univ Cyprus, Med Sch, Nicosia, Cyprus. [Farmakis, Dimitrios; Filippatos, Gerasimos S.] Univ Athens, Athens Univ Hosp Attikon, Dept Cardiol, Heart Failure Unit, Athens, Greece. [Gialafos, Elias] Henry Dunant Hosp, Heart Failure & Prevent Cardiol Sect, Dept Cardiol 2, Athens, Greece. [Limongelli, Giuseppe] Univ Campania Luigi Vanvitelll, Dept Cardiothorac Sci, Monaldi Hosp, AORN Colli,Ctr Ric Cardiovasc,Osped Monaldi, Naples, Italy. [Limongelli, Giuseppe] UCL Inst Cardiovasc Sci, London, England. [Linhart, Ales] Charles Univ Prague, Gen Univ Hosp, Dept Cardiovasc Med, Dept Med 2, Prague, Czech Republic. [Lyon, Alexander R.] Imperial Coll London, Natl Heart & Lung Inst, London, England. [Lyon, Alexander R.] Royal Brompton Hosp, London, England. [Maksimovic, Ruzica] Clin Ctr Serbia, Ctr Radiol & Magnet Resonance Imaging, Belgrade, Serbia. [Milicic, Davor] Univ Zagreb, Univ Hosp Ctr Zagreb, Dept Cardiovasc Dis, Zagreb, Croatia. [Noutsias, Michel] Martin Luther Univ Halle Wittenberg, Univ Hosp Halle, Div Cardiol Angiol & Intens Med Care, Dept Internal Med 3,Mid German Heart Ctr, Halle, Germany. [Oto, Ali] Hacettepe Univ, Dept Cardiol, Fac Med, Ankara, Turkey. [Oto, Oztekin] Dokuz Eylul Univ, Fac Med, Dept Cardiovasc Surg, Izmir, Turkey. [Pavlovic, Sinisa U.] Clin Ctr Serbia, Pacemaker Ctr, Belgrade, Serbia. [Piepoli, Massimo F.] Guglielmo da Saliceto Hosp, Cardiol, Heart Failure Unit, Piacenza, Italy. [Rosano, Giuseppe M. C.] IRCCS San Raffaele, Dept Med Sci, Rome, Italy. [Rosano, Giuseppe M. C.] Univ London, Cardiol Clin Acad Grp, St Georges Hosp NHS Trust, London, England. [Seggewiss, Hubert] Klinikum Wurzburg Mitte, Med Klin, Kardiol & Internist Intensivmed, Wurzburg, Germany. [Seferovic, Jelena R.] Harvard Med Sch, Brigham & Womens Hosp, Cardiovasc Div, Boston, MA 02115 USA. [Seferovic, Jelena R.] Univ Belgrade, Clin Ctr Serbia, Clin Endocrinol Diabet & Metab Disorders, Belgrade, Serbia. [Ruschitzka, Frank] Univ Heart Ctr, Dept Cardiol, Zurich, Switzerland. [Celutkiene, Jelena] Vilnius Univ, Clin Cardiac & Vasc Dis, Inst Clin Med, Fac Med, Vilnius, Lithuania. [Celutkiene, Jelena] State Res Inst Ctr Innovat Med, Vilnius, Lithuania. [Jaarsma, Tiny] Linkoping Univ, Fac Hlth Sci, Dept Social & Welf Studies, Linkoping, Sweden. [Mueller, Christian] Univ Basel, Univ Hosp Basel, CRIB, Basel, Switzerland. [Mueller, Christian] Univ Basel, Univ Hosp Basel, Dept Cardiol, Basel, Switzerland. [Moura, Brenda] Ctr Hosp Sao Joao, Cardiol Dept, Porto, Portugal. [Hill, Loreena] Queens Univ Belfast, Sch Nursing & Midwifery, Belfast, Antrim, North Ireland. [Volterrani, Maurizio] IRCCS San Raffaele Pisana, Dept Cardiol, Rome, Italy. [Lopatin, Yuri] Volgograd State Med Univ, Reg Cardiol Ctr Volgograd, Volgograd, Russia. [Metra, Marco] Univ Brescia, Dept Med & Surg Specialties Radiol Sci & Publ Hlt, Cardiol, Brescia, Italy. [Backs, Johannes] Heidelberg Univ, Dept Mol Cardiol & Epigenet, Heidelberg, Germany. [Backs, Johannes] DZHK German Ctr Cardiovasc Res, Partner Site Heidelberg Mannheim, Heidelberg, Germany. [Mullens, Wilfried] Hasselt Univ, Fac Med & Life Sci, BIOMED Biomed Res Inst, Diepenbeek, Belgium. [Mullens, Wilfried] Ziekenhuis Oost Limburg, Dept Cardiol, Genk, Belgium. [Chioncel, Ovidiu] Univ Med & Pharm Carol Davila, Bucharest, Romania. [Chioncel, Ovidiu] Emergency Inst Cardiovasc Dis Prof CC Iliescu, Bucharest, Romania. [de Boer, Rudolf A.] Univ Groningen, Univ Med Ctr Groningen, Dept Cardiol, Groningen, Netherlands. [Anker, Stefan] Dept Cardiol CVK, Div Cardiol & Metab, Berlin, Germany. [Anker, Stefan] Berlin Brandenburg Ctr Regenerat Therapies BCRT, Berlin, Germany. [Anker, Stefan] DZHK German Ctr Cardiovasc Res, Partner Site Berlin, Berlin, Germany. [Rapezzi, Claudio] Alma Mater Studiorum Univ Bologna, Dept Expt Diagnost & Specialty Med, Cardiol, Bologna, Italy. [Coats, Andrew J. s] Monash Univ, Clayton, Vic, Australia. [Coats, Andrew J. s] Univ Warwick, Coventry, W Midlands, England. [Coats, Andrew J. s] IRCCS San Raffaele Pisana, Ctr Clin & Expt Med, Pharmacol, Rome, Italy. [Coats, Andrew J. s] St Georges Univ London, London, England. [Tschoepes, Carsten] Charite Univ Med Berlin, Dept Cardiol, Deutsch Zentrum Herz Kreislauf Forsch DZHK Berlin, Berlin Brandenburg Ctr Regenerat Therapies, Campus Virchow Klinikum, Berlin, Germany. | Keywords: | Heart failure; Dilated cardiomyopathy; Hypertrophic cardiomyopathy; Restrictive cardiomyopathy; Peripartum cardiomyopathy; Epidemiology; Natural history; Pathophysiology; Management;Heart failure; Dilated cardiomyopathy; Hypertrophic cardiomyopathy; Restrictive cardiomyopathy; Peripartum cardiomyopathy; Epidemiology; Natural history; Pathophysiology; Management | Document URI: | http://hdl.handle.net/1942/28996 | ISSN: | 1388-9842 | e-ISSN: | 1879-0844 | DOI: | 10.1002/ejhf.1461 | ISI #: | 000471307000006 | Rights: | 2019 The Authors : European Journal of Heart Failure 2019 European Society of Cardiology | Category: | A1 | Type: | Journal Contribution | Validations: | ecoom 2020 |
Appears in Collections: | Research publications |
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